Yes your children have a 50% chance of inheriting the gene from you but only your son would be affected by it. If I was you I would probably get tested and then worry about the implications if you need to...........cross one bridge at a time!

If you carry the gene defect then it would be really worthwhile seeing a genetic counsellor - they will be able to tell you all about your options and answer your questions much better than I can! As for messing with mother nature - well that is a decision you have to make and a genetic counsellor will help you with that. It's not uncommon in families who carry serious genetic disorders. Alternatively you may be able to screen for the gene irrespective of sex, thereby choosing not to implant affected embryos. Not saying you should do this, but these options are available.